Retinitis
Pigmentosa
The retina lies
in the back of the eye and is a multi-layered tissue which detects visual
images and transmits them to the brain. Retinitis pigmentosa (RP) refers
to a group of related diseases which tend to run in families and cause
slow but progressive loss of vision. In retinitis pigmentosa, there
is gradual destruction of some of the nervous sensors in the retina.
The first symptoms usually occur in youth or young adulthood, although
it may be first seen at any age. Retinitis pigmentosa causes night blindness
and loss of side vision. In normal persons, the visual system adjusts
to darkness after a short period of time. People with night blindness
adjust to darkness very slowly, or not at all. Due to the loss of side
vision (peripheral vision) in patients with retinitis pigmentosa, mobility
becomes more difficult.
Most forms of retinitis pigmentosa are inherited. Different patterns
of heredity are associated with different degrees of progression. An
attempt to know more about how severely the disease has affected other
family members may help predict how a specific person might ultimately
be afflicted, though variability exists within each family. Such knowledge
is also helpful in making decisions about such things as marriage, family
and occupation.
In general, there is no specific treatment. Recent research suggests
that some patients may benefit from certain kinds of vitamin therapy.
But these studies are not conclusive. Much research is directed toward
solving this problem. Periodic examinations by an eye doctor are advised.
It is important to keep in mind that patients with retinitis pigmentosa
may develop other treatable disease, such as glaucoman or cataracts.
Low vision aids may be prescribed. In some cases, retinitis pigmentosa
may be associated with other disease processes which might need evaluation
by other medical specialists.
Despite visual impairment, the many rehabilitative services that are
available today allow patients with retinitis pigmentosa to live meaningful
and rewarding lives.
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